KMID : 0978920170180010044
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Korean Journal of Clinical Geriatrics 2017 Volume.18 No. 1 p.44 ~ p.47
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Cretzfeldt-Jakob Disease Mimicking Progressive Supranuclear Palsy Presenting With Supranuclear Gaze Palsy and Early Falling
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Kim Jin-Hee
Kim Ji-Yeon Kwon Do-Young Choi Won-Suk
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Abstract
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Sporadic Creutzfeldt-Jakob disease (sCJD) is fatal prion disease typically characterized by rapid progressive dementia often associated with various movement disorders such as myoclonus and ataxia. However, atypical manifestations and varied clinical courses make timely diagnosis of sCJD difficult. Here we describe probable sCJD patients with gait disturbance and early falling as an initial clinical manifestations mimicking progressive supranuclear palsy (PSP).
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KEYWORD
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Cretzfeldt-Jakob disease, Progressive supranuclear pasly, Atypical parkinsonism, Rapidly progressive dementia
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