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KMID : 0978920170180010044
Korean Journal of Clinical Geriatrics
2017 Volume.18 No. 1 p.44 ~ p.47
Cretzfeldt-Jakob Disease Mimicking Progressive Supranuclear Palsy Presenting With Supranuclear Gaze Palsy and Early Falling
Kim Jin-Hee

Kim Ji-Yeon
Kwon Do-Young
Choi Won-Suk
Abstract
Sporadic Creutzfeldt-Jakob disease (sCJD) is fatal prion disease typically characterized by rapid progressive dementia often associated with various movement disorders such as myoclonus and ataxia. However, atypical manifestations and varied clinical courses make timely diagnosis of sCJD difficult. Here we describe probable sCJD patients with gait disturbance and early falling as an initial clinical manifestations mimicking progressive supranuclear palsy (PSP).
KEYWORD
Cretzfeldt-Jakob disease, Progressive supranuclear pasly, Atypical parkinsonism, Rapidly progressive dementia
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